Indwara zidasanzwe: ibintu, izina, bidasanzwe

Anonim

Nubwo iterambere rya siyansi na tekinike ryimiterere yuburyo bwose kamere ishoboye gutungura, bike ntabwo ihinduka munsi. Kandi kurutonde rwibitekerezo bitangaje, amabanga ntabwo umurongo wanyuma ufata umubiri wumuntu. Insanganyamatsiko y'ibikoresho ni indwara zidasanzwe, vuga ku ndwara zidasanzwe z'indwara zidasanzwe kandi zidasanzwe no gukomeza gushyira abaganga mu isuzuma ryapfuye.

Ikibazo

Umugabo mubuzima bwose akomeje kwiyongera no guhinduka - uruhinja nyuma yimyaka mirongo azahinduka sidins yashinze imizi yumusaza, keretse, byanze bikunze, ibyago bitunguranye bitabaho. Ariko bibaho kugirango abantu bashobore gutanga igihe ntarengwa. Turimo kuvuga ku ndwara yitwa "Proteria", biganisha ku gusaza imburagihe impinduramamanuka ku mpinduka zihuza uruhu rw'imiryango n'inzego zimbere.

Kugaragara ku gahato, byasobanuwe bwa mbere mu byatinze bya XIX, bitera inenge mu miterere ya ADN, kubera ko umubiri utangira gushira vuba. Nubwo, nk'urugero rw'abarwayi bafite iki cyo gusuzuma, abana bakunze gutangwa n'abana, kubera ihohoterwa rikorerwa muri gereza, ni nk'umusaza muto urengeje imyaka 13, indwara ni gushobora kwigaragaza mumyaka yakuze.

Kubwibyo, abahanga batanga ubwoko 2 bwiterambere: Hatchinson-Gilford Syndrome - Mubana na Syndrome na Werner - mubantu bakuru. Mu kimenyetso cya mbere, indwara ntirazwe, ariko ivuka kubera ihinduka ry'imiterere idasanzwe mu gushyiraho urusoro cyangwa mugihe cyegereje ingirabuzimafatizo. Mu kimenyetso cya kabiri, umurage ni automosomal-resosomal. Ni ukuvuga, kugirango syndrome ya Werner yigaragaze, kuba isene yangiritse kubabyeyi bombi irakenewe.

Fibrodisplazia

Uruhu rushobora kuba flabby kandi rukarira mbere yigihe nko mubarwayi bafite igare ryibimuga. Kandi bibaho ko imitsi, imitsi namagambo bigoramye kuri igufwa ryamagufwa, nkuko bibaye mubantu bafite isuzuma rya "Fibrodisplasia". Muri uru rubanza, indwara idasanzwe yatewe n'indwara ikomeye ya genetique, hari ukwishyuza buhoro buhoro ingirangingo yoroshye. Nk'itegeko, indwara, imanza z'ubwa mbere zanditswe mu binyejana bya XVII-XVII-XVII-XVII, iboneka mu bana bafite genome yahindutse afite imyaka 9-10, nyuma yo gutera imbere.

Fibrodisplas ni sporadic - kwigaragaza mu manza zitaruye. Nubwo abanzi bamenyeshejwe, aho ibisekuruza byinshi byatsinzwe. Hashingiwe kuri ibi bintu, abahanga banzuye ko indwara ishoboye kuragwa n'ihame ryiganjemo yigenga, kohereza ababyeyi kugira bandu gutesha agaciro abana.

Fibrodisplas ni ugutera imbere cyane (Fop) itandukanye no gutera imbere gukomeza kandi bitera kurenga ku kugenda kwa Skeleton no gupfa hakiri kare - abarwayi benshi bapfuye mu nkingo akiri muto akana.

Ubukungu bwa Encephalitis

Mu 1917, inzobere muri Otirishiya, Kontantin von Economo, yasobanuye bwa mbere amashami ashyira mu gaciro, iyo umuntu, areba abasinzi, akomeza kuvuga kandi azi ibibera. Muri icyo gihe, umubiri wose utwikiriye ubumuga, niyo mpamvu abarwayi baretse gusubiza ibiterankunga byo hanze. Indwara yahamagawe mu rwego rwo guha icyubahiro yavumbuwe - icyorezo cy'ubukungu mu bukungu ubukungu bw'ubukungu. Nanone, yakundaga kwitabwaho "indwara isinziriye" (kutitiranya na gariyamoshi nyafurika, uwatwaye ari we vets).

Ubukungu bwa Encephalitis

Birashimishije kubona ko abaganga bagena icyateye Econayo Encephalitis kuburyo idashobora. Bamwe babonaga ko virusi itazwi, abandi - badasubiza umuhanga mu kamaro k'umubiri, biganisha ku kurimbuka k'ubwonko. Byagaragaje ko kwandura bibaye mugihe uhamagaye umurwayi cyangwa ibitonyanga. Niba mugihe cyicyiciro gikaze cyindwara, birangwa no gusinzira, umuntu ntazapfa, hanyuma nyuma yigihe gito azakira.

Ubuvuzi bwihariye ntabwo bwari bworoshye. Nibyo, ubuzima busigaye bwo kwiyegurira buzababazwa nibigaragaza Partinteplititic ParkinsonIm, ifatwa nkaho ari parkinson. Ongeraho urutonde rwarwo "Indwara zanditse" zihagaze kandi kubera icyorezo, kwihuta mu 1915-1926 ku isi, indwara nini yo kwandura econoomo Encephalitis itagikosowe.

Keroderima

Benshi mu batuye umubumbe bamenyereye ko izuba rimwe na rimwe rishobora kuganisha ku buryo "uruhu rurarira." Muri icyo gihe, kwibagirwa imirasire ya ultraviolet irashobora kandi kuganisha ku kugaragara kwa kanseri mbi. Noneho ni bangahe bashobora kutagira ingaruka ku buzima munsi yimirasire y'amanywa, bigenwa nubushake bwumubiri. Ariko ufite indwara idasanzwe yitwa "keroderma pigment" kubera ubwinshi bwimirasire ya ultraviolet amahirwe yo kutarinda munsi yizuba bidahari na gato.

Imvururu ni umurage kandi bwa mbere kwigaragaza mubana bafite imyaka 2-3. Igisubizo gihinduka isura igira ingaruka za UV yumurangizo wuruhu, gutwika no gutwika ushoboye kuganisha ku byabayeho kanseri gutsindwa kwa kanseri gutsindwa kwa kanseri gutsindwa kwa kanseri gutsindwa kwa kanseri gutsindwa kwa kanseri. Impamvu y'indwara - mu maboko yo gusanwa ya poroteyine z'ibikorwa byagabanijwe bya Enzymes, Kuringaniza ingaruka mbi za ultrasoviolet ku ruhu. No mubarwayi kubera urumuri rw'izuba barababara n'amaso ababara.

HyperrtricHose

Iyo abahagarariye kubuntu kureba abantu, umusatsi ukura mu rukebwe cyangwa mumato ni asanzwe. Iyo isura yumuntu ishushanyije ubwanwa, ubwanwa cyangwa byose hamwe, ibi ntabwo aribyo bitandukanye. Ariko niba imikurire irenze umusatsi, kandi itarasama hasi n'imyaka, igaragara mu bice byumubiri, bikaba bidasanzwe (urugero, inyuma, inyuma, noneho bimaze kuba indwara bita "hyperitrihoz".

Hyperrtrichose igabanijwemo channetal kandi iboneka. Mu rubanza rwa mbere, iyo mpamvu ihinduka umurage w'ingirabuzimafatizo zifite inenge ku muntu ku giti cye - kubera kwimurwa kwa transfer, ubu bwoko bukunze kugaragara mu bahungu. Ku bijyanye na patologiya, bibaho kandi mu bakobwa akenshi, kandi abahungu kubera kurenga ku ruganda rw'akazi k'urubanza rwimbere, cyane cyane igitsina. Ariko, izindi ndwara, nka spinal dystrophy cyangwa imitsi ya anorexia, kimwe no gukomeretsa umutwe, inzara cyangwa ubumuga bwa kivuni cyangwa impengamiro cyangwa impinja zivugarane zirashoboye kubwimpamvu.

Trimentlaminaria

Impumuro idashimishije ituruka kumubiri nyuma yimbaraga zikomeye zumubiri, ntamuntu utunguwe. Nibyo, kandi "bivugishije" ibibazo nkibi muburyo bworoshye - birasabwa gusa kwiyuhagira cyangwa gukaraba munsi yo kwiyuhagira. Ariko amahitamo nkaya yo gukuraho "ambre" ntabwo akwiriye abarwayi bafite isuzuma rya Trimithylanuria, rizwi kandi nka "Syndrome ya Flay Shome". Iri zina ntabwo ryunguka - umwuka uranga "uruzi" ukomoka ku ndwara, rimwe na rimwe hamwe "inoti".

Indwara zituruka kubera ukurenga ku mwijima, kubera ko enzyme ireka kubyara, itandukanya na trimeidembemine n-ogisi, ihinduka impumuro mbi. Imvururu akenshi zivuka kubera inenge kurwego rwa gene. Ariko, rimwe na rimwe kubura enzyme bitera ingaruka zo kurwanya abahangange zangiza, ibiyobyabwenge byibasiye kanseri, kimwe na nikotine.

Allergie

Mu buryo nk'ubwo, abantu bafite keroderim, bamaze kuganirwaho haruguru mu gutoranya "indwara zidasanzwe z'isi", uruhu ntirushobora gutwara imvura ya ultrasolet no mu mibabaro ikonje (ubukonje), nkuko bigaragara Mu izina, uruhu rwuruhu ntirukwihanganira ingaruka zubushyuhe buke. Igisubizo ku bukonje kigaragara kubera gusohokana gutunguranye kw'imigozi igana mu buryo bw'ibibanza bitukura bifite umuriro utwika no kurasa. Kubyimba kw'ingingo za "Frozen" akenshi zikosorwa.

Nk'itegeko, igishishwa giterwa na allergie ku ruhu nyuma yo guhagarika ubushyuhe bwo hasi butakiri icumi-indi minota. Ariko, ibibazo byanditswe mugihe kurakara nyuma yiminsi 5-7 kandi biherekejwe no kubaho kwabice cyangwa gukuramo. Nanone, indwara irashobora gutera asima. Kandi imitekerereze ikabije cyane muburyo bwuruhu hamwe nigihuru gisenya imigezi yimbere, bituma bigora guhumeka.

Ubukonje urticariya bwarazwe nihame ryigenga ryigenga kandi rifitanye isano no gutandukana - ubwoko nk'ubwo bwitwa "umuryango". Indwara ya membranes ya mastocrate (selile yera), iboneka kandi iterwa n'ingaruka zibintu bifatika. Ibimenyetso birashobora kwigaragaza kumyaka iyo ari yo yose, ariko akenshi uhura n'urupfu rw'abagore hejuru ya 30.

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