Ubuzima
Abo mu gihe ntibyagaragaye mubyishimo byumugabo. Kuri bo, yari igisimba, abasohoka hamwe n'abatandukanije na benshi. Impano zo mu buryo bworoshye, inzovu yubuntu ku buntu ku butaka yabaye ingwate y'indwara ye kandi imyaka myinshi yinjije mu myaka ibiri yishyize munsi. Ikinyabupfura nubugome bwabantu ntabwo byahinduye Yosefu mumirongo itabifitiye uburenganzira. Kugeza mu gihe cye kirangiye, yari umuntu wishimye ufunguye, nubwo adafite ikinyarwanda hanze, yari mwiza cyane.Mu bwana n'urubyiruko
Joseph Cary Merrick yavutse ku ya 5 Kanama 1862 mu burasirazuba bw'Ubwongereza - mu mujyi wa Leicester. Yosefu yari mukuru kuva abana batatu. Murumuna we, Alliam Arthur yapfuye azize amatafu afite imyaka ine, kandi murumunawe Marion Eliza yavuka afite ubumuga kandi apfa mu myaka 24. Nk'uko byatangajwe na Autobiographical Icyitonderwa Crick, ubumuga bwatangiye kwigaragaza afite imyaka itanu. Nyina Mariya Jane Pottrton - umwarimu wishuri ryo ku cyumweru - yapfuye mu 1873. Umwaka utaha, se Joseph Rockley Merrick yajyanye undi mugore mu mugore we.
Umuryango wa Merrick wizeraga ko ububi bwagaragaye biturutse ku byabaye, byabayeho hamwe na Mary Jane mbere gato yo kuvuka. Kuba umugore utwite, umugore yari afite ubwoba ku kindi cyinzovu isabiriza. Ikinyoma Inararibonye y'amarangamutima y'ababyeyi zigaragarira ku isura y'abana bataravuka, yari igipimo mu Bwongereza mu kinyejana cya 19. Merrick yajugunye ishuri afite imyaka 13. Ubuzima bwe n'umubyeyi we na papa bahindukiriye ikuzimu, kuko nta n'umwe wigeze amwishimira.
Ibyitwanwa n'icyifuzo cyo gusubiramo umuhungu mu ijosi rya Rockley byita ku bagabo Joseph Jr. yakira uruhushya rw'umucuruzi wo mu muhanda. Ariko, igitekerezo cyarananiranye. Abashobora kuba abakiriya bafite ubwoba bakiriye isura ya Merrik. Nyuma yimyaka ibiri, Yozefu, Yozefu yashoboye kubona akazi ku ruganda rw'itabi, ariko guhindura ukuboko kw'iburyo ku buryo mu myaka itatu atagishoboye kuzuza igipimo cy'umusaruro w'itabi. Mu 1877, se yakubise Yozefu, ava mu rugo ubuziraherezo.
Mu 1884, Merrick yatangiye gukora muri sirusi yo kwerekana Tom Norman. Hafi ya 1886 muri 1486 muri Victorian Ubwongereza "Erekana Freaks" byatangajwe hanze y'amategeko. Merrik yoherejwe gutembera mu Burayi. Amaze kumushuka maze ajugunya umukoresha nta ngabo i Buruseli, Yosefu yagombaga kujya kwa Essex, hanyuma ava muri gari ya moshi agera i Londres. Ntabwo bizwi uburyo ubuzima bwumuntu - inzovu yaba yarateje imbere iyo umuganga uzwi cyane wa TriVZ, wize indwara ya crick mugihe cyimyaka mike, ntabwo yibujije Yosefu ibitaro bya Royal Londres.
Icyamamare
Itangazamakuru ryahinduye igisimba kandi buhenze mubiranga London. Ibikoresho byasohotse mu binyamakuru byahinduye mu buryo bwibanze ku mibanire rusange na Merrik. Amateka ye yubuzima bwe yakoze ku mutima wa ndetse n'umwamikazi w'Ubwongereza - Alexandra Danish. Umugezi, uherekejwe na saloph, yasuye Yozefu inshuro nyinshi. Mu nyandiko y'ububiko bwamanutse kugeza na n'ubu, havugwa ko umugore yashoboraga kuvugana na Merrita.
Yosefu yize hamwe numutunzi w'imbere w'isi - akesha ubufasha bwa Trivizi, yashoboye gusura amakinamizi n'imurikagurisha. Yasomye byinshi, kandi mu myaka yatinze nanditse Prosse na insire. Izwi cyane ku buryo mu byiciro byanyuma byubuzima, Merrica mubisanzwe ikora ukuboko kw'ibumoso gusa. Iri hitaguriwe ntizarinze impano Yozefu yo gukusanya icyitegererezo cya katedrali kuva ku mpapuro, nyuma yaje guha abaforomo n'abaganga.
Impeshyi 1887, 1888 na 1889, umuntu winzovu yamaze ibyumweru bibiri muri kamere. Kugira ngo abuze Merrika kubera ibitekerezo bitari ngombwa kuri Yawak ukomoka mu mujyi, Yozefu yakuwe mu gutwara umwenda ufunze cyane. Abagabo ntibakoze kuri iyi ngingo na gato. Yishimiye kuva mu mujyi wa Londi. Ubumwe na Kamere namwe namwe. Yaruhutse umubiri mwinshi nk'ubugingo.
Urupfu
Imyaka yanyuma yubuzima bwinzovu yumuntu yabereye mubitaro bya Royal Londres. Abakozi b'ikigo cy'ubuvuzi bita kuri Merrita kandi bakoze ibishoboka byose kugirango umugabo yorohewe. Reka no mugihe gito, ariko Joseph aracyashoboye kumva ari umunyamuryango wa societe yuzuye. Kuzenguruka ntibikiriho igisimba muri cyo. Bamufashe nk'umwe: ntibimaze kureba Koso, ntibakubita urutoki. Yosefu yashoboraga kugenda atuje kandi avugana nabarwayi nabaganga. Mubindi bintu, abantu bakunze kuza mu bihe biteye agahinda.
Merrick yapfuye ku ya 11 Mata 1890 (imyaka 27). Ku munsi w'urupfu, yagumye mu cyumba cye, anyura mu cyumba cy'abaganga, aryama mu mwanya utambitse (kubera ko yandikaga umutwe yemerewe gusinzira gusa). Ku myaka ya 13h00, umutwe uremereye urenze ijosi rinini, kandi inzovu yapfuye azize asphyxia.
Indwara n'impamvu zayo
Dukurikije imigani ya kera y'Abagereki, inyanja ya Protea inyanja ifite ubushobozi bwo guhindura imiterere y'umubiri we. Iyi ngingo yimukiye ivuye mu migani mubuzima busanzwe. Mu gusobanura igezweho, ibintu byiswe - syndrome ya proteus. Gutandukana nkibi ni indwara ivukanwa no gutangiza selile. Kugeza ubu, iterambere ryinshi rirashoboka gukumira. Ku nshuro ya mbere iyi ndwara muri 1979, Michael Cohen yasobanuye mu mirimo ye ya siyansi.
Abana bavutse bafite syndrome yintangarugero mumyaka ya mbere baratera imbere nkabantu bose basanzwe. Ibimenyetso byuburwayi bitangira kugaragaza nyuma yimyaka 2 yubuzima nyuma. Ibimenyetso biratandukanye cyane. Ikintu nyamukuru ni ugukura mubice byihariye byumubiri mubunini bunini. Uruhu, amagufwa, imitsi, gushira tissue, lymphatike n'amaraso bigira uruhare muri gahunda. Kurugero, ingingo zirashobora kwiyongera, ijosi, umutwe, mu maso. Impinduka zisanzwe zidasanzwe. Gukura kw'impapuro biganisha ku kibazo, muri byo: kuvunika, indwara zingingo n'imitsi y'ingingo, imitsi y'ingingo, guhagarika umutima, kubyimba.
Ibindi syndrome de syndrome de syndrome: Uruhu Neoplasm, guhindura pigmentation, anomalies yimiterere yintoki namaguru. Syndrome ya Proteus irasuzumwa hashingiwe kubimenyetso byo hanze. Nk'uburyo, ubugenzuzi bugaragara bwuzuzwa no gukoresha uburyohe nk'ubwo bw'ibikoresho nk'ikirere, MRI na CT. Ikizamini cya genetike gikorwa kugirango cyemeze kwanyuma kwisuzumisha, mugihe amaraso yumurwayi hamwe ningero zamagambo ya hypertrophie iperereza.
Nta ndwara idafite ubuvuzi. Ubuvuzi bugamije gukosorwa ibimenyetso no gukumira ingorane. Amayeri yo "feri" yindwara yatoranijwe kugiti cye. Indwara ubwayo ntabwo igira ingaruka ku iterambere ryubwenge. Nukuri, amagufwa no gukura kw'ingingo birashobora guteza ibibazo bya Neurologiya no guhindura ibintu. Mubindi bintu, abarwayi bafite ibibazo muguhitamo imyenda ninkweto, kimwe no kurangiza ubuhanga bwibanze bwo kwikorera (kurya, gukora nabi). Kubera inenge zo hanze, abantu barwaye iyi ndwara biragoye kumenyera muri sosiyete no gushaka umwanya wabo mubuzima.
Ishusho mu muco
- Ikinamico y'Abanyamerika Bernard Amaraso "Umuntu w'inzovu" mu musaruro wa muyobozi Jack Ho %ssa (1978);
- Verisiyo ya tereviziyo ya Broadway Kina "Umugabo-Inzovu" (1982);
- Movie David David Lynch "Umuntu w'inzovu" hamwe na John yakomeretse mu ruhare rwa Yozefu na Anthony Hopkins mu ruhare rwa Frederick Trivza (1980);
- Filime ya Albert na Allen Hughes "kuva ikuzimu", aho umuntu w'inzovu igaragara cyane (2001);
- Opera ya Composer Composer Laurent Plurerian "Joseph, inzovu" ishingiye kuri Licretto y'umwimerere Eric Nonna muri Daniel Megishani (2002);
- Clip Michael Jackson "Syireke wenyine" (1989). Muri videwo, umuhanzi yabyinnye iruhande rwa skeleton ya Merrik;
- Kunyunyuza inkuru ya Joseph birahari muri film ngufi Pablo Larkuen "inzovu";
- Umuroma Espagne Umwanditsi Felix H. Palma - "Igihe cyigihe" (2008);
- Televiziyo ya documentaire "umuvumo w'inzovu" (2003);
- Mu gihembwe cya kabiri cya tereviziyo y'Ubwongereza "Umuhanda wa Ripper", Joseph na Fredrick trivz yabaye abantu benshi (2013);
- Umugabo w'inzovu yagaragaye mu gice cya Cleveland y'Abanyamerika yerekana kaseti ya kaseti (2013);
- Ishusho ya Yozefu yakoreshejwe mu kwamamaza chip ya Nik Naks.