Zvirwere zvinokatyamadza: Zvimiro, zita, zvisingawanzo

Anonim

Kunyangwe kufambira mberi kwesainzi uye kwehunyanzvi kwemarudzi ese ezvinyadzo izvo zvisikwa zvinokwanisa kushamisika, zvishoma hazvisi zvishoma. Uye mune rondedzero yekufungidzira kunoshamisa, zvakavanzika kwete mutsara wekupedzisira unogara mumuviri wemunhu. Dingindira rezvinyorwa ndizvo zvakashata zvirwere, taura nezvezvakarukwa zvezvirwere zvisina kujairika uye zvichiramba kuendesa varapi mukuongororwa kwakafa.

Problity

Munhu muhupenyu hwese anoramba achikura uye achinja - achangozvarwa mushure memakumi emakore achazova matanda emurume wekare, kunze kwekunge, dambudziko rakangoerekana raitika. Asi zvinoitika kuitira kuti vanhu vagone kuita yekupedzisira nguva yekupedzisira. Tiri kutaura nezve chirwere chinonzi "preria", izvo zvinotungamira mukukwegura kwekutanga kwemuviri neanoshandura shanduko mukuonekwa kweganda uye nhengo dzemukati.

Kumuzopamhi kweanopokana, kwakatanga kurondedzerwa mumakore emaxix makore, anotungamira kuremara muchimiro cheDNA, semhedzisiro iyo muviri inotanga kukurumidza kupera. Kunyangwe, semuenzaniso wevarwere vane kuongororwa uku, vana vanowanzo kupihwa nevana avo, nekuda kwekutyora mumakore ekuzvarwa vachiri mudiki uye havawanzo kuve kwenguva refu kupfuura makore 13, chirwere ichi chiri kugona kuzviratidza mumakore akura.

Naizvozvo, masayendisiti anogovera maviri akasiyana ekufambira mberi: Hatchinon-gilford syndrome - muvana uye Werner syndrome - mune vakuru. Mune yekutanga embodiment, hosha yacho haina kugarwa nhaka, asi inomuka semhedzisiro yekuzvisarudzira mukuumbwa kwehumambo kana panguva yekuibva kwemazita emuzinda. Mune yechipiri embodiment, nhaka izere-inodzokororwa. Ndokunge, kuitira kuti murwere weWerner azviratidze, iko kuvapo kweGene yakakuvadzwa kubva kune vese vabereki vanodiwa.

Fibrodisplazia

Ganda rinogona kunge riri kubhururuka uye kuchema pamberi penguva savarwere newiricheya. Uye zvinoitika kuti mhasuru, tendon uye ligaments dzakaomesa mamiriro efupa, sezviri kuitika muvanhu vane kuongororwa kwe "fibrodisplasia". Mune ino kesi, chirwere chisingawanzo chakakonzerwa neakakomba genetic kusagadzikana, pane zvishoma nezvishoma kusarudzika kwematehwe akapfava. Semutemo, chirwere ichi, nyaya dzekutanga kunyoreswa panguva yeXvii-XVII-XVII-XVII-XVII-XVIE nemakore ane makore makumi mapfumbamwe nemashanu, mushure meizvozvo zvichiramba kufambira mberi.

Fibrodispliss iri Spordic - inoratidzira pachako mumatare ari ega. Kunyangwe zvatangira zvakanyorwa, umo zvizvarwa zvakati wandei zvakakundwa. Zvichienderana nezvazviri izvi, masayendisiti akagumisa kuti chirwere ichi chinogona kugarwa nhaka nemitemo yekuzvitutumadza, kutapurirana nevabereki kubva mukuvanzika kwevana.

Iyo fibrodisplis is a precisiting kufambira mberi (fop) inosiyana mukufambira mberi nekuenderera mberi nekupwanya kwekufamba kweiyo skeleton uye kutanga kwevarwere

Encephalitis hupfumi

Muna 1917, imwe neurologist kubva kuAustria, Konstantin von Vezvehupfumi, vanotanga kurondedzera madhipatimendi epakati nepakati, kana munhu akatarisa pakurara, anoramba achiziva kuti chii chiri kuitika. Panguva imwe chete, muviri wese unovhara mitezo mitezo, ndosaka vanorwara vachisiya kuti vapindure mukukurudzira kwekunze. Iyo chirwere ichi yakadaidzwa mukuremekedza iyo discover - Epidemic Economic Economic Economiclitis. Zvakare, aigara achitaurwa se "chirwere chekurara" (kwete kuvhiringidzwa neAfrican Tribanosomozoomaoma iri muHaha Mhezi).

Encephalitis hupfumi

Zvinokosha kuziva kuti vanachiremba vanoratidza chikonzero cheEconalo encephalitis saka vaisakwanisa. Vamwe vakaona vhiri risingazivikanwe, vamwe - mhinduro isina kujairika yemuviri, inotungamira mukuparadzwa kwehuropi. Izvo zvakaratidza kuti hutachiona hunoitika kana uchibata murwere kana madonhwe-madonhwe. Kana panguva yechikamu chakakomba chechirwere, chakangoratidzwa nemamiriro ekurara, munhu haazofi, mushure mekunge chinguva chichapora.

Kurapa kwakakosha hakuna kugadzirwa. Chokwadi, hupenyu hwakasara hwekuzvipira huchatambura nekuratidzwa kwePasitonichac Parkinsonism, iyo inobatwawo zvakafanana nechirwere cheParkinson. Wedzera kusiririsa kweiyo rondedzero "zvirwere zvakatemwa" zvinomira uye mushure medenda, kumhanyisa muna 1915-1926 munyika, hutachiona hwakakura hwakadaro hazvo hwehupfumi hachisisiri yakatarwa.

Keroderma

Vazhinji vavagari vepasi vanojaira chokwadi chekuti kuwana kwenguva refu muzuva kunogona kutungamira mune zvakanyanyisa kuitika kune chokwadi chekuti "ganda rino misodzi." Panguva imwecheteyo, kukanganwa kuti radilolet radiation inogona zvakare kutungamira mukubuda kwevakashata canksant. Uyezve vanhu vazhinji vanogona kunge vasina kukuvadza hutano pasi pemarara emisikanzwa, vakatsanangurwa neparutivi rwemuviri wayo. Asi iwe une chirwere chisingawanzo chinonzi "keroderma pigment" nekuda kwekuwedzera kwekunzwa kune Ultraviolet radiation mukana wekuve pasina dziviriro pasi pezuva isipo zvachose.

Iko kusagadzikana kunhaka uye kekutanga kunoratidza pachako muvana makore 2-3. Mhedzisiro yacho inova kutaridzika iri pasi pesimba reUV ravheni rekutsamwa kweganda, rinopisa uye kuzvimba kunogona kutungamira kuchingo chegomarara. Chikonzero chechirwere - mune yakagadziridzwa DNA yemapuroteni eiyo chiitiko chakaderedzwa che enzymes, kuunganidza zvakashata zvakanakira Ultraviolet pamasero eganda. Zvakare mumarwere nekuda kwechiedza chezuva kutambudzika uye maziso anotambura.

Hyperricosis

Kana vamiriri vemaonero emahara emaonero evanhu, bvudzi rinokura mumiroto kana mumakwikwi ndiwo maitiro. Kana chiso chomurume chinoshatisa ndebvu, 'ngazvirege kusukwa kana zvese pamwe, uku hakusi kutsauka zvachose. Asi kana kukura kwebvudzi, uye kusiri kuenderana nepasi uye zera, kunoonekwa mumativi emuviri, kwazvinenge zvisina kujairika (semuenzaniso, kumashure, etc.), zvobva zvatova nezvechirwere inonzi "hyperitrihoz".

Hyperricosis yakakamurwa kuita curdenital uye inowanikwa. Muchiitiko chekutanga, chikonzero chinova nhaka yemarudzi akaremara kubva pamubereki - nekuda kweshoko rekutamisa, iyi mhando inowanzo kuratidzwa muvakomana. Kana zvasvika pakuwana pathology, zvinoitikawo muvasikana mune zvakawanda, uye vakomana nekuda kwekutyora kwebasa remberi, kunyanya bonde. Nekudaro, zvimwe zvirwere, zvakadai se musina wenzure kana nerve anorexia, pamwe nekukuvara kwemusoro, nzara kana kusarongeka kwekusarongeka kunokwanisa zvikonzero.

Trimethaminoria

Kunhuhwirira kusingafadzi kunouya kubva mumuviri mushure mekukosha kwakakura mumuviri, pasina kushamisika. Ehe, uye "takabatwa" dambudziko rakadaro nenzira yakapusa - inongoda kugeza kana kugeza pasi pekugeza. Asi sarudzo dzakadaro dzekubvisa peculiar "ambi" hazvina kukodzera kune varwere vane kuongororwa kwetrimetherminuria, vanozivikanwa zvakare se "hove kunhuhwirira". Iri zita harina kubatsira - hunhu "hwerwizi" hunobva pakurwara, dzimwe nguva uine zvimwe "zvinyorwa" kuora.

Mawere anomuka nekuda kwekutyorwa kwechiropa, nekuda kwekuti enzyme inoregedzwa kuti riwedzere, kupatsanura trimethlamine n-oxide sounhu rakashata, ramba kugadzirwa. Kusagadzikana kazhinji kunowanzo kumuka nekuda kwekuremara pazera reGadzira. Nekudaro, dzimwe nguva kushomeka kweiyo enzyme kunokanganisa kukanganiswa kweanoparadza maAndidepressants, zvimwe zvinodhaka nekenza, pamwe nicotine.

Kutonhora allergy

Saizvozvowo, vanhu vane kero yeKeroderm, uyo akatokurukurwa pamusoro mukusarudzwa kwe "chirwere chinoshamisa chenyika", ganda risingakwanisi kuwa nekudonha kweiyo allergies (kutonhora kurwara), zvakajeka Kunze kwezita, chifukidziro cheganda hachitsigire kukanganiswa kwekushisa kwakaderera. Kuita kwacho kune chando kunoonekwa nekuda kwekukurumidza kubviswa kwehistamine makosi mune fomu yerudzi rakatsvuka zvine hungichimbi uye inovhara. Kuzvimba kwe "mitezo ye" chando "inowanzogadziriswa.

Semutemo, kupaza kunokonzerwa neyakaipisisa kuita paganda mushure mekutaurwa kwekutaridzika kwekunze-tembiricha hakusisiri gumi nemaviri-maminitsi. Nekudaro, nyaya dzakanyorwa kana kutsamwiswa kwapera mushure memazuva 5-7 uye kunoperekedzwa nekuitika kwemabhururu kana kubhururuka. Zvakare, chirwere ichi chinogona kukonzera asthma. Uye kunyanyisa acute maitiro mukufananidza neganda rashests kunomutsa kuzvimba kwemberi dzemukati, izvo zvinoita kuti zviome kufema.

Iyo inotonhora urticaria inogarwa nhaka neinodhonza musimboti uye inosanganisirwa nedzinza rejitari - rudzi rwakadaro rwechirwere runonzi "mhuri". Dambudziko muMettocyte membranes (chena masero eropa), izvo zvinowanikwa uye zvinokonzerwa nekukanganisa kwezvinhu zvemuviri. Zviratidzo zvinogona kuzviratidza chero pazera ripi neripi, asi kazhinji vanotambura nerufu rwevakadzi vanopfuura makumi matatu.

Verenga zvimwe